XLH patients can be affected by tooth abscesses in both deciduous and permanent dentition. The disease results in a diminished barrier to the exterior of the tooth, with cracks in the thin enamel, extended pulp horns, and abnormal formation of the dentine, allowing bacteria and infections to enter the tooth pulp chamber without any visible damage to the tooth.4,11
In an international online survey of parents/caregivers of 90 children with XLH aged 0 to 18 years, it was found that 51% of children had dental abscesses.1
Spontaneous abscesses appear as a result of bacterial invasion into the expanded pulp chamber via the thin and fissured enamel and abnormally mineralised and malformed dentine.4,11
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